Idiopathic Pulmonary Fibrosis

Texas Pulmonary Institute, with locations in Port Arthur and Beaumont, Texas, specializes in the diagnosis and treatment of Pulmonary Fibrosis which literally means scarring of the lungs. The scarring occurs in the interstitium, which is the lung tissue that provides the scaffolding (support structure) for the alveoli (air sacs). Fibrosis thickens the interstitium, making the air sacs stiff so that they are unable to fully expand and hold as much air as they normally should. This thickening also limits passage of oxygen through the wall of the alveoli into the bloodstream. Over time, fibrosis can worsen to the point that patients may need supplemental oxygen to raise low blood oxygen levels, relieve shortness of breath, and improve exercise ability. Texas Pulmonary Institute is specialized in a wide variety of breathing disorders. Make an appointment today at Texas Pulmonary Institute by calling 409-401-5864.

Symptoms of IPF

The main symptom of IPF is shortness of breath with activity, which exists in almost everyone as the disease progresses.

  • In fact, in IPF, shortness of breath often limits physical activity. People with IPF may have to slow down, rest and recover throughout an activity or even give up physical activities they once did with ease.
  • Many people with IPF notice they have the most trouble walking quickly, climbing stairs, or going up inclines.
  • About 85% of people with IPF will have a cough. The most frequently occurring symptoms of IPF (shortness of breath, cough and fatigue)

High Risk

  • IPF is usually diagnosed in people between the ages of 50 and 80 years.
  • IPF is very uncommon in people under the age of 50 years.
  • Men are at higher risk than women.
  • A past or current history of smoking cigarettes or working in a dusty environment also increases the risk of developing IPF.
  • IPF sometimes runs in families, and there are several genes associated with its development

Possible Treatment

  • Pirfenidone and nintedanib are two anti-fibrotic drugs that are used for the long-term treatment of IPF. Antifibrotic means that the drugs block scarring. Scar formation in the lungs is complex and involves many different types of cells.
  • Oxygen therapy can relieve shortness of breath by increasing blood oxygen levels.
  • Pulmonary rehabilitation is a safe way to exercise under supervision. pulmonary rehabilitation program can help you improve your energy level, reduce your shortness of breath, give you a better understanding of your IPF.

More Pulmonary Fibrosis Information

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